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La cicatrisation et la déformation du tissu pulmonaire entraîne un dérèglement significatif de l'échange gazeux et de la fonction ventilatoire. L'une des méthodes de classification consiste à diviser les maladies pulmonaires interstitielles en deux groupes selon qu'elles soient 1) de causes connues ou 2) des causes inconnues. Chaque groupe peut ensuite être sous-divisé selon la présence ou l'absence de granulomes."],"label":[],"synonym":[],"obsolete":false,"prefixIRI":null,"subClassOf":[],"xref":null,"inScheme":[],"created":null,"modified":null,"memberOf":[],"altLabelXl":[],"hiddenLabelXl":[],"parents":[],"prefLabelXl":[],"isInActiveScheme":[null],"isInActiveCollection":[],"properties":{"https://data.bioontology.org/metadata/def/prefLabel":["20000042"],"http://purl.bioontology.org/ontology/MDRFRE/SMQ_ALGO":["N"],"http://www.w3.org/1999/02/22-rdf-syntax-ns#type":["http://www.w3.org/2002/07/owl#Class"],"http://bioportal.bioontology.org/ontologies/umls/tui":["T185"],"http://purl.bioontology.org/ontology/MDRFRE/SMQ_LEVEL":["1"],"http://www.w3.org/2004/02/skos/core#notation":["20000042"],"http://purl.bioontology.org/ontology/MDRFRE/SMQ_STATUS":["A"],"http://purl.bioontology.org/ontology/MDRFRE/SMQ_SOURCE":["Not provided"],"http://bioportal.bioontology.org/ontologies/umls/hasSTY":["http://purl.bioontology.org/ontology/STY/T185"],"http://bioportal.bioontology.org/ontologies/umls/cui":["C1869044"],"http://www.w3.org/2004/02/skos/core#prefLabel":["Maladie pulmonaire interstitielle (SMQ)"],"http://www.w3.org/2004/02/skos/core#definition":["Les maladies pulmonaires interstitielles sont un groupe hétérogène d'états impliquant les parois alvéolaires et tissus péri-alvéolaires. 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