{"id":"http://purl.bioontology.org/ontology/MDRFRE/20000130","prefLabel":"Hypertension pulmonaire (SMQ)","notation":"20000130","semanticType":["http://purl.bioontology.org/ontology/STY/T185"],"cui":["C1963999"],"definition":["Le 5ème Symposium Mondial sur l'Hypertension Pulmonaire (HP), 2013, établit une nouvelle classification de l'hypertension pulmonaire. Une nouvelle définition de l'hypertension pulmonaire a été publiée en 2015. Celle-ci a un impact sur les paramètres d'identification des cas pour la SMQ Hypertension pulmonaire (SMQ). Il a alors été décidé de modifier la SMQ Hypertension pulmonaire (SMQ). Une nouvelle définition et de nouveaux critères d'inclusion/exclusion dans la SMQ ont été établis, sur les conclusion du 5ème Symposium sur l'HP, de la Force d'Intervention Commune pour le Diagnostic et le Traitement de l'HP de la Société Européenne de Cardiologie (ESC) et de la Société Respiratoire Européenne (ERS). La liste de termes de cette SMQ a été mise a jour en conséquence et ses termes soumis aux essais. L'HP avait été définie comme une pression artérielle pulmonaire moyenne de repos (mPAP) > 25 mm Hg ou une mPAP d'effort > 30 mm Hg. Le sous-groupe d'HP connu comme hypertension artérielle pulmonaire (PAH) ajoute le critère suivant: la pression artérielle pulmonaire bloquée doit être = 15 mm Hg. Quelques définitions incluent également la résistance vasculaire pulmonaire (PVR), exigeant qu'elle soit =2 ou 3 unités Wood. Les faiblesses potentielles de la définition précédente sont liées au fait que le niveau type et la position de l'effort n'ont pas été précisés. De plus, la pression artérielle pulmonaire d'effort normale (PAP) varie avec l'âge. La clarification de la définition basée sur l'évidence disponible a été un important objectif de la recommandation 2015 de l'ESC/ERS. La nouvelle définition de l'HP est une pression moyenne de repos de l'artère pulmonaire (mPAP) = 25 mm Hg. Des études supplémentaires sont nécessaires pour mieux déterminer l'évolution naturelle des patients présentant une mPAP de 21 à 24 mm Hg. Les critères d'effort et de résistance vasculaire pulmonaire (PVR) devraient être éliminés. Une mPAP de repos de 8 à 20 mm Hg devrait être considérée normale."],"label":[],"synonym":[],"obsolete":false,"prefixIRI":null,"subClassOf":[],"xref":null,"inScheme":[],"created":null,"modified":null,"memberOf":[],"altLabelXl":[],"hiddenLabelXl":[],"parents":[],"prefLabelXl":[],"isInActiveScheme":[null],"isInActiveCollection":[],"properties":{"https://data.bioontology.org/metadata/def/prefLabel":["20000130"],"http://purl.bioontology.org/ontology/MDRFRE/SMQ_ALGO":["N"],"http://www.w3.org/1999/02/22-rdf-syntax-ns#type":["http://www.w3.org/2002/07/owl#Class"],"http://bioportal.bioontology.org/ontologies/umls/tui":["T185"],"http://purl.bioontology.org/ontology/MDRFRE/SMQ_LEVEL":["1"],"http://www.w3.org/2004/02/skos/core#notation":["20000130"],"http://purl.bioontology.org/ontology/MDRFRE/SMQ_STATUS":["A"],"http://purl.bioontology.org/ontology/MDRFRE/SMQ_SOURCE":["Diagnosis and Assessment of Pulmonary Arterial Hypertension. Journal of the American College of Cardiology Vol. 54, No. 1, Suppl S.; Updated Clinical Classification of Pulmonary Hypertension. Journal of the American College of Cardiology Vol. 54, No. 1, Suppl S. Guidelines for the diagnosis and treatment of pulmonary hypertension. European Heart Journal (2009) 30, 2493-2537; Assessment of right ventricular volumes and ejection fraction by echocardiography: from geometric approximations to realistic shapes. 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