{"id":"http://purl.bioontology.org/ontology/MDRFRE/20000131","prefLabel":"Syndrome de Guillain-Barré (SMQ)","notation":"20000131","semanticType":["http://purl.bioontology.org/ontology/STY/T185"],"cui":["C1964000"],"definition":["Le syndrome de Guillain-Barré (SGB) est une polyradiculonévrite démyélinisante inflammatoire aiguë à médiation immunitaire. Cet état suit habituellement une maladie virale ou mycoplasmique affectant les voies respiratoires supérieures ou les voies digestives. D'autres événements antécédents incluent certaines vaccinations. Il est probable que les réponses immunitaires dirigées contre les organismes infectants ont une réactivité croisée avec les tissus neuraux, dont la membrane de surface de la cellule de Schwann (à l'origine de la polyradiculonévrite démyélinisante inflammatoire aiguë) ou la membrane axonale (formes aiguës axonales). Le SGB est caractérisé par : faiblesse ou paralysie affectant plus d'un membre, généralement de façon symétrique ; perte du réflexe tendineux ; et protéine du liquide céphalo-rachidien (LCR) augmentée, sans pléocytose. Parmi les autres caractéristiques, on citera : atteinte motrice et sensorielle ; atteinte de nerf facial ou crânien ; et signes électrophysiologiques de démyélinisation. La forme aiguë du SGB évolue rapidement, en quelques heures à quelques jours, atteignant en général un niveau de faiblesse maximal dans les quatre semaines. L'état est classé comme polyradiculonévrite démyélinisante inflammatoire chronique si les symptômes du patient continuent à évoluer au-delà de quatre semaines ou en cas de rechutes. Pour une polyradiculonévrite démyélinisante inflammatoire chronique, le niveau d'incapacité physique maximum survient généralement dans les deux mois."],"label":[],"synonym":[],"obsolete":false,"prefixIRI":null,"subClassOf":[],"xref":null,"inScheme":[],"created":null,"modified":null,"memberOf":[],"altLabelXl":[],"hiddenLabelXl":[],"parents":[],"prefLabelXl":[],"isInActiveScheme":[null],"isInActiveCollection":[],"properties":{"https://data.bioontology.org/metadata/def/prefLabel":["20000131"],"http://purl.bioontology.org/ontology/MDRFRE/SMQ_ALGO":["N"],"http://www.w3.org/1999/02/22-rdf-syntax-ns#type":["http://www.w3.org/2002/07/owl#Class"],"http://bioportal.bioontology.org/ontologies/umls/tui":["T185"],"http://purl.bioontology.org/ontology/MDRFRE/SMQ_LEVEL":["1"],"http://purl.bioontology.org/ontology/MDRFRE/SOS":["REMARQUE : Les cas pertinents peuvent être extraits sans l'algorithme ; cependant, son application peut être utile lorsque la recherche à portée large identifie un grand nombre de cas. Consulter la documentation du Groupe de travail du CIOMS pour des détails sur l'algorithme et les listes des termes des catégories. Catégorie A (portée étroite) : termes représentant le SGB et les sous-types. Catégorie B (portée large) : les signes et symptômes très répandus des cas bien documentés du syndrome de Guillain-Barré et ses variantes, sur la base des résultats de tests. La plupart des termes se rapportent aux paresthésies, aux hypoesthésies et aux neuropathies. Catégorie C (portée large) : les signes, symptômes et analyses biologiques à visée diagnostique répandus, sur la base des résultats de tests. Catégorie D (portée large) : les signes, symptômes et analyses biologiques à visée diagnostique moins répandus provenant des résultats de tests, ainsi que les signes, symptômes et analyses biologiques à visée diagnostique possiblement constatés en présence du syndrome de Guillain-Barré et de ses variantes, mais qui n'ont pas été observés dans les bases de données testées. Les cas sélectionnés pour revue incluront tous les cas remplissant l'un des critères ci-dessous : 1) au moins un des PT de catégorie A (portée étroite) ou 2) tous les cas rapportant au moins deux PT de catégorie B ou 3) tous les cas rapportant au moins un PT de catégorie B et au moins un PT de catégorie C ou 4) tous les cas rapportant au moins un PT de chacune des catégories B, C et D. Pour certains médicaments ayant beaucoup de cas avec des termes tels que paresthésie, hypoesthésie et faiblesse musculaire, on risque d'obtenir davantage de \" bruit \" avec l'algorithme 2B et 1B + 1C. Pour ces produits, il est recommandé d'utiliser l'algorithme 1B + 1C + 1D, qui peut éliminer beaucoup du \" bruit \" produisant des faux positifs."],"http://www.w3.org/2004/02/skos/core#notation":["20000131"],"http://purl.bioontology.org/ontology/MDRFRE/SMQ_STATUS":["A"],"http://purl.bioontology.org/ontology/MDRFRE/SMQ_SOURCE":["1) Textbook of Clinical Neurology, 2nd Edition, pp1085-1089, 2003. 2) Cecil Textbook of Medicine, 22nd Edition, pp 2379-2381, 2004. 3) Harrison's Internal Medicine, 16th Edition, pp 2513-2518, 2005. 4) Ferri F. Guillain-Barre syndrome. Ferri's Clinical Advisor: Instant Diagnosis and Treatment, 2006 ed. Available at http://home.mdconsult.com/das/book/58437071-2/view/1302. 5) Cha-Kim A. Guillain-Barr? syndrome. eMedicine. Available at http://www.emedicine.com/pmr/topic48.htm. Accessed May 22, 2006. 6) Aarli JA. Role of Cytokines in Neurologic Disorders. Current Medicinal Chemistry. 2003; 10:1931-1937. 7) Stedman's Medical Dictionary. 26th edition. Williams & Wilkins. Baltimore, MD; 1995."],"http://bioportal.bioontology.org/ontologies/umls/hasSTY":["http://purl.bioontology.org/ontology/STY/T185"],"http://bioportal.bioontology.org/ontologies/umls/cui":["C1964000"],"http://www.w3.org/2004/02/skos/core#prefLabel":["Syndrome de Guillain-Barré (SMQ)"],"http://www.w3.org/2004/02/skos/core#definition":["Le syndrome de Guillain-Barré (SGB) est une polyradiculonévrite démyélinisante inflammatoire aiguë à médiation immunitaire. Cet état suit habituellement une maladie virale ou mycoplasmique affectant les voies respiratoires supérieures ou les voies digestives. D'autres événements antécédents incluent certaines vaccinations. Il est probable que les réponses immunitaires dirigées contre les organismes infectants ont une réactivité croisée avec les tissus neuraux, dont la membrane de surface de la cellule de Schwann (à l'origine de la polyradiculonévrite démyélinisante inflammatoire aiguë) ou la membrane axonale (formes aiguës axonales). Le SGB est caractérisé par : faiblesse ou paralysie affectant plus d'un membre, généralement de façon symétrique ; perte du réflexe tendineux ; et protéine du liquide céphalo-rachidien (LCR) augmentée, sans pléocytose. Parmi les autres caractéristiques, on citera : atteinte motrice et sensorielle ; atteinte de nerf facial ou crânien ; et signes électrophysiologiques de démyélinisation. La forme aiguë du SGB évolue rapidement, en quelques heures à quelques jours, atteignant en général un niveau de faiblesse maximal dans les quatre semaines. L'état est classé comme polyradiculonévrite démyélinisante inflammatoire chronique si les symptômes du patient continuent à évoluer au-delà de quatre semaines ou en cas de rechutes. Pour une polyradiculonévrite démyélinisante inflammatoire chronique, le niveau d'incapacité physique maximum survient généralement dans les deux 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